Chronic Thromboembolic Pulmonary Hypertension (CTEPH)
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Symptoms and risk factors of this blood clot in the lungs
Expert Heart & Vascular Care
Getting the care you need starts with seeing one of our heart or vascular specialists.
Chronic thromboembolic pulmonary hypertension (CTEPH) is characterized by high blood pressure in the pulmonary arteries (the blood vessels in the lungs) that lasts six months or longer. It’s a rare type of pulmonary hypertension in which a blood clot in the lung, known as a pulmonary embolism, forms scar-like tissue and blocks blood flow.
This blood clot increases pressure in the pulmonary arteries and strains the right side of the heart, which becomes overworked and enlarged. If left untreated, CTEPH can lead to heart failure.
However, if caught early, it may be managed with medication or cured with a surgery called pulmonary thromboendarterectomy (PTE). The specialists in our Pulmonary Hypertension Clinic will work with you to develop an effective treatment plan.
What are the symptoms of CTEPH?
CTEPH symptoms are similar to those of asthma, chronic obstructive pulmonary disease (COPD) and heart failure.
Some symptoms you may experience if you have CTEPH include:
- Chest pain
- Coughing up blood
- Fatigue
- Shortness of breath, lightheadedness or fainting with physical activity
What are the risk factors for CTEPH?
A pulmonary embolism can trigger CTEPH. Up to 1 in 25 people who have had a pulmonary embolism—even those who were treated with blood thinners—develop CTEPH. Having multiple pulmonary embolisms can increase your CTEPH risk.
Certain medical conditions can increase your risk as well, such as:
- Blood clotting disorders
- Having had your spleen removed
- Chronic inflammatory conditions such as inflammatory bowel disease
- Cancer
- Infected pacemaker or defibrillator wire
Tests
Angiogram (Angiography)
An angiogram is a special X-ray taken as a special dye is injected through a thin, flexible tube called a catheter to detect blockages or aneurysms in blood vessels.
Cardiac Catheterization
Cardiac catheterization is a minimally invasive way to diagnose and treat a variety of heart and vascular conditions by guiding thin, flexible tubes called catheters through blood vessels to problem areas.
Chest X-ray
Chest X-rays use a small dose of radiation to create pictures of the structures inside the chest, including the lungs, heart and chest wall.
Computerized Tomography (CT) Scan
The cardiac computed tomography scan, or cardiac CT, uses X-rays to create three-dimensional images of your heart and blood vessels.
Treatments
Our heart and vascular teams work together and with other specialties to develop and implement individualized plans to treat a wide variety of conditions. This could include medication or more advanced treatments.
For a list of MedStar Health pulmonology specialists, click here.
Physicians
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